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Duchenne's Muscular Dystrophy and heart disease
Patients with Duchenne's Muscular Dystrophy are at a high risk for both arrhythmias and heart failure and should be followed (and treated) agressively.
The heart failure occurs as a "dilated cardiomyopathy", causing "systolic dysfunction":
http://www.cardiachealth.org/ca-blog/heart-function-failure/ (look here for systolic dysfunction).
Treatment often includes angiotensin-converting enzyme (ACE) inhibitors or angiotensin receptor blockers (ARBs)plus Alpha-receptor blockade is clear for cardiomyopathy patients without muscular dystrophy, and there is no reason to avoid this standard regimen in muscular dystrophy patients:
Likewise, arrhythmias if present should be evaluated with monitoring and other testing such as a Holter monitor and possibly another EP study:
Lots of information for you, but I hope this helps,
Ask Doctor T. Blog
My 12 yr old son (140cm, 38kg) had a recent episode last month of sudden fainting, hit the back of his head on the concrete at high speed. Was unconscious for under a minute. Went to emergency via ambulance and his ECG showed QT prolonged 492ms. Question 1.Could the knock on his head of caused this ? (he did have a previous episode of unconsciousness but it was...